2Department of Haematology, Antwerp University Hospital, Antwerp, Belgium
3Division Gynaecologic Oncology, Department of Obstetrics and Gynaecology, Multidisciplinary Breast Clinic, Antwerp University Hospital, Antwerp, Belgium
4Faculty of Medicine and Health Sciences, University of Antwerp, Antwerp, Belgium; Biobank, Antwerp University Hospital, Antwerp, Belgium
5Faculty of Medicine and Health Sciences, University of Antwerp, Antwerp, Belgium; Department of Haematology, Antwerp University Hospital, Antwerp, Belgium
Abstract
Mycosis fungoides (MF) is an indolent form of non-Hodgkin lymphoma and the most common type of primary cutaneous T-cell lymphoma. The overall incidence of MF is approximately 4 per 1 million. Involvement of the vulva by MF is extremely rare, with only seven reported cases in the literature. At the vulva, it is mainly a metastatic lesion and rarely a primary malignancy. We describe a case of vulvar MF and discuss the previous cases. The presentation can easily be confused with benign skin disorders. A vulvar lesion can reflect a systemic disease. When a patient consults for a vulvar lesion it is therefore important not only to look at the vulva but also to examine her in and ask general questions. In a patient with a vulvar mass and cutaneous lesions on other locations MF should be considered in the differential diagnosis. (NCI-2020-0014.R1)